The definition of Pulmonary arterial hypertension (PAH)

A disorder primarily of small pulmonary arteries which results in a progressive rise in pulmonary vascular resistance and right ventricular failure. There are several forms of PAH including Idiopathic Pulmonary Arterial Hypertension (IPAH) and Associated PAH related to a range of disease processes, including connective tissue disease, congenital heart disease, HIV infection and sickle-cell disease.

If you are a patient and you have any questions about these definitions or how they apply to you, please contact your healthcare provider.